Spontaneous rupture of primary splenic angiosarcoma: A case report

Xu,Botao; Xie,Xiaona; Zhou,Xiong; Zhai,Menghe; Yang,Wenjun

doi:10.3892/ol.2015.3714

Spontaneous rupture of primary splenic angiosarcoma: A case report

Authors:
- Botao Xu
- Xiaona Xie
- Xiong Zhou
- Menghe Zhai
- Wenjun Yang
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Affiliations: Division of General Surgery, First Affiliated Hospital of Wenzhou Medical University, Wenzhou, Zhejiang, P.R. China, Pulmonary Division, Wenzhou Traditional Chinese Medicine Hospital, Wenzhou, Zhejiang, P.R. China
Published online on: September 16, 2015 https://doi.org/10.3892/ol.2015.3714
Pages: 3271-3273

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Abstract

Primary angiosarcoma of the spleen is an extremely rare malignant neoplasm of vascular origin that often has a poor prognosis. The majority of cases presents with splenic rupture and hemorrhage. The present study retrospectively analyzed the case of 77-year-old female who presented with diffuse abdominal pain and distension. During laparotomy, a huge actively bleeding spleen was identified and a splenectomy was performed. Since an accurate diagnosis could not be achieved by abdominal computed tomography, a pathological examination was performed. The patient and the family refused post‑operative adjuvant chemotherapy and radiation therapy. The patient succumbed to uncontrolled hemorrhagic shock and lung metastases at 2 weeks post-surgery.

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