Cystic nephroma treated with nephron‑sparing technique: A case report

Baio,Raffaele; Spiezia,Nicola; Schettini,Manlio

doi:10.3892/mco.2021.2271

Cystic nephroma treated with nephron‑sparing technique: A case report

Authors:
- Raffaele Baio
- Nicola Spiezia
- Manlio Schettini
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Affiliations: Department of Urology, University of Salerno, I-84081 Salerno, Italy, Department of Urology, Lourdes Clinic, I-80040 Massa di Somma, Italy
Published online on: March 23, 2021 https://doi.org/10.3892/mco.2021.2271
Article Number: 109
Copyright: © Baio et al. This is an open access article distributed under the terms of Creative Commons Attribution License.

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Abstract

Multilocular cystic nephroma is a rare benign kidney tumor, which is typically characterized by a unilateral, multicystic renal mass without solid elements. Cystic nephroma has a bimodal distribution and two‑thirds of tumors involve children aged between 3 months and 2 years, with male predominance; a second peak affects the age group >30 years old, in which females are predominantly affected. The incidence rate for this rare tumor in patients aged 5‑30 years is only 5%. The present study reports a case of a 31‑year‑old woman affected by a multilocular cystic nephroma in the upper pole of the right kidney, with direct tumor extension into the renal pelvis through a calyx. After a partial nephrectomy on the patient, the pathological examination confirmed a multilocular cystic nephroma in the right renal specimens.

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