Rare presentation of peripheral primitive neuroectodermal tumor in the maxilla and mandible: A report of two cases

Wang,Chao; Qiu,Tian-Tian; Yu,Xin-Feng; Xuan,Min; Gu,Quan-Quan; Qian,Wei; Zhang,Min-Ming

doi:10.3892/ol.2014.2219

August-2014 Volume 8 Issue 2

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August-2014 Volume 8 Issue 2

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Rare presentation of peripheral primitive neuroectodermal tumor in the maxilla and mandible: A report of two cases

Authors:
- Chao Wang
- Tian-Tian Qiu
- Xin-Feng Yu
- Min Xuan
- Quan-Quan Gu
- Wei Qian
- Min-Ming Zhang
View Affiliations / Copyright

Affiliations: Department of Radiology, The Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou, Zhejiang 310009, P.R. China
Pages: 615-619
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Published online on: June 3, 2014

https://doi.org/10.3892/ol.2014.2219
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Abstract

Peripheral primitive neuroectodermal tumor (pPNET) is a rare and highly malignant undifferentiated tumor, which presents in infants and young adults. pPNETs in the head and neck region are uncommon and have a varying incidence of occurrence. Peripheral PNETs of the maxilla and mandible are particularly rare. At present, only 16 cases of pPNET of the maxilla and 13 cases of pPNET of the mandible have been reported. The present study describes a case of pPNET of the maxilla in a 16‑year‑old male and a case of pPNET of the mandible in another 16‑year‑old male. The present study reports the radiological findings and the clinical courses of the two patients.

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Journals

International Journal of Molecular Medicine

International Journal of Oncology

Molecular Medicine Reports

Oncology Reports

Experimental and Therapeutic Medicine

Oncology Letters

Biomedical Reports

Molecular and Clinical Oncology

World Academy of Sciences Journal

International Journal of Functional Nutrition

International Journal of Epigenetics

Medicine International

Rare presentation of peripheral primitive neuroectodermal tumor in the maxilla and mandible: A report of two cases

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