Gastric cancer following a liver transplantation for glycogen storage disease type Ia (von Gierke disease): A case report

  • Authors:
    • Hua Xiao
    • Jianmin Bian
    • Lei Zhang
    • Zhaoming Wang
    • Aixing Ding
  • View Affiliations

  • Published online on: October 9, 2014     https://doi.org/10.3892/ol.2014.2599
  • Pages: 2803-2805
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Abstract

Glycogen storage disease type Ia (GSD‑Ia; also termed von Gierke disease) is an inherited metabolic disorder resulting from a glucose‑6‑phosphatase deficiency. Liver transplantation is considered to be the most effective treatment for GSD‑Ia patients. In the present study, the case of a patient with GSD‑Ia who received a liver transplantation at 17 years of age is presented. During the 12 years following transplantation, the patient's quality of life markedly improved. However, recently, the patient was diagnosed with de novo gastric cancer following a biopsy. Thus, a total gastrectomy with lymph node dissection was performed and the tumor was histologically determined to be a poorly differentiated adenocarcinoma (histopathological stage, pT4N1M0). The patient recovered well and was discharged on postoperative day 10 without any complications. To the best of our knowledge, this is the first case of de novo gastric cancer in a patient with GSD‑Ia to be reported.
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December-2014
Volume 8 Issue 6

Print ISSN: 1792-1074
Online ISSN:1792-1082

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Spandidos Publications style
Xiao H, Bian J, Zhang L, Wang Z and Ding A: Gastric cancer following a liver transplantation for glycogen storage disease type Ia (von Gierke disease): A case report. Oncol Lett 8: 2803-2805, 2014
APA
Xiao, H., Bian, J., Zhang, L., Wang, Z., & Ding, A. (2014). Gastric cancer following a liver transplantation for glycogen storage disease type Ia (von Gierke disease): A case report. Oncology Letters, 8, 2803-2805. https://doi.org/10.3892/ol.2014.2599
MLA
Xiao, H., Bian, J., Zhang, L., Wang, Z., Ding, A."Gastric cancer following a liver transplantation for glycogen storage disease type Ia (von Gierke disease): A case report". Oncology Letters 8.6 (2014): 2803-2805.
Chicago
Xiao, H., Bian, J., Zhang, L., Wang, Z., Ding, A."Gastric cancer following a liver transplantation for glycogen storage disease type Ia (von Gierke disease): A case report". Oncology Letters 8, no. 6 (2014): 2803-2805. https://doi.org/10.3892/ol.2014.2599