Pigmented paravenous retinochoroidal atrophy (Review)

Huang,Hou‑Bin; Zhang,Yi‑Xin

doi:10.3892/etm.2014.1648

Pigmented paravenous retinochoroidal atrophy (Review)

Authors:
- Hou‑Bin Huang
- Yi‑Xin Zhang
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Affiliations: Department of Ophthalmology, The General Hospital of Chinese PLA, Beijing 100853, P.R. China, Department of Ophthalmology, Hainan Branch of General Hospital of PLA, Sanya, Hainan 572013, P.R. China
Published online on: March 28, 2014 https://doi.org/10.3892/etm.2014.1648
Pages: 1439-1445

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Abstract

Pigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon disease characterized by perivenous aggregations of pigment clumps associated with peripapillary and radial zones of retinochoroidal atrophy that are distributed along the retinal veins. Patients are usually asymptomatic and the disease process is non‑progressive or slow and subtly progressive. It is commonly bilateral and symmetric. The cause of the condition may be unknown or idiopathic, although a dysgenetic, degenerative, hereditary etiology or even an inflammatory cause has been hypothesized. A non‑inflammatory cause is referred to as primary, while inflammation‑associated PPRCA is referred to as secondary or pseudo PPRCA. The present study reviewed and summarized the features of PPRCA.

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