Pure sensory Guillain‑Barré syndrome: A case report and review of the literature

Yang,Jingjing; Huan,Mingming; Jiang,Huajun; Song,Chunli; Zhong,Lin; Liang,Zhanhua

doi:10.3892/etm.2014.1955

November-2014 Volume 8 Issue 5

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November-2014 Volume 8 Issue 5

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Case Report

Pure sensory Guillain‑Barré syndrome: A case report and review of the literature

Authors:
- Jingjing Yang
- Mingming Huan
- Huajun Jiang
- Chunli Song
- Lin Zhong
- Zhanhua Liang
View Affiliations / Copyright

Affiliations: Department of Neurology, First Affiliated Hospital of Dalian Medical University, Dalian, Liaoning 116011, P.R. China, Department of Orthopedics, First Affiliated Hospital of Dalian Medical University, Dalian, Liaoning 116011, P.R. China, Department of Pathology, First Affiliated Hospital of Dalian Medical University, Dalian, Liaoning 116011, P.R. China
Pages: 1397-1401
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Published online on: September 11, 2014

https://doi.org/10.3892/etm.2014.1955
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Abstract

Sensory Guillain‑Barré syndrome (GBS) is an acute demyelinating neuropathy that presents clinically with involvement of the sensory peripheral nerve only. To date, <10 cases of pure sensory GBS have been reported; thus, the clinical and pathological features of sensory variant GBS are yet to be well characterized. The current study reports the case of a 43‑year‑old female that presented with acute, symmetric and monophasic sensory neuropathy, without motor weakness. Patient history, clinical examination, routine nerve conduction studies and sural nerve biopsy were reviewed. All the observations were consistent with a diagnosis of pure sensory GBS. In particular, the pathological features of the sural nerve biopsy revealed that the form of regenerated nerve fibers have complete structure of myelinated nerve fascicles, and these myelinated nerve fibers are thicker than other parts of the biopsy. The patient received small‑dose (20 mg/day) prednisone initially, but without any benefit. Satisfactory improvements were observed with one course of intravenous immunoglobulin.

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Journals

International Journal of Molecular Medicine

International Journal of Oncology

Molecular Medicine Reports

Oncology Reports

Experimental and Therapeutic Medicine

Oncology Letters

Biomedical Reports

Molecular and Clinical Oncology

World Academy of Sciences Journal

International Journal of Functional Nutrition

International Journal of Epigenetics

Medicine International

Pure sensory Guillain‑Barré syndrome: A case report and review of the literature

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