Solitary extrapulmonary lymphangioleiomyomatosis of the liver: A case report and literature review

Fu,Weiwei; Li,Yujun; Li,Hong; Yang,Ping; Xing,Xiaoming

doi:10.3892/etm.2016.3502

Solitary extrapulmonary lymphangioleiomyomatosis of the liver: A case report and literature review

Authors:
- Weiwei Fu
- Yujun Li
- Hong Li
- Ping Yang
- Xiaoming Xing
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Affiliations: Department of Pathology, The Affiliated Hospital of Qingdao Medical College, Qingdao University, Qingdao, Shandong 266003, P.R. China, Department of Pathology, The Affiliated Yantai Yuhuangding Hospital of Qingdao University, Yantai, Shandong 264000, P.R. China
Published online on: July 5, 2016 https://doi.org/10.3892/etm.2016.3502
Pages: 1499-1502

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Abstract

Lymphangioleiomyomatosis (LAM) is a progressive disorder of unknown etiology that predominantly affects the lungs, and the resulting respiratory failure can be fatal. Extrapulmonary LAM is a rare disease that often occurs concurrently with pulmonary LAM. Usually, extrapulmonary LAM presents as a localized, well‑circumscribed mass. Due to the rare occurrence of extrapulmonary LAM and its atypical location, extrapulmonary LAM is often difficult to diagnose prior to surgery. The present study describes the clinicopathological features of primary liver LAM in a 26‑year‑old woman. To the best of our knowledge, the present study presents the first case of a primary solitary extrapulmonary form of LAM in the liver.

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