Primary intra‑abdominal desmoid fibromatosis associated with familial adenomatous polyposis: A case report

Zhang,Lei; Zheng,Yaotun; Yu,Xiaoqian; Yu,Kang; Zhu,Shengjie

doi:10.3892/etm.2023.12007

Primary intra‑abdominal desmoid fibromatosis associated with familial adenomatous polyposis: A case report

Authors:
- Lei Zhang
- Yaotun Zheng
- Xiaoqian Yu
- Kang Yu
- Shengjie Zhu
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Affiliations: Department of Hepatobiliary Surgery, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China, Department of Anesthesia, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China, Department of Obstetrics, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China, Department of Research and Development, Tianjin Lianchuang Technology Development Co., Ltd., Tianjin 300000, P.R. China, Department of Oncology, Weihai Central Hospital, Weihai, Shandong 264200, P.R. China
Published online on: May 10, 2023 https://doi.org/10.3892/etm.2023.12007
Article Number: 308
Copyright: © Zhang et al. This is an open access article distributed under the terms of Creative Commons Attribution License.

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Abstract

Desmoid fibromatosis (DF) is a clonal proliferative disorder of myofibroblasts, which arises, with a low incidence, in soft tissue, including within the abdomen. The incidence of DF is associated with familial adenomatous polyposis (FAP), and is more common following FAP surgery. It is rare for a patient to make his/her first visit to hospital due to DF symptoms associated with FAP. In the present report, a case of mesenteric DF associated with FAP is described. This case also had incomplete intestinal obstruction due to DF. By summarizing previous studies examining DF and FAP treatment, combined with the disease characteristics of this patient, the clinical treatment strategy for DF associated with FAP was explored.

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