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Print ISSN: 1792-0981 Online ISSN: 1792-1015
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February-2024 Volume 27 Issue 2

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Case Report Open Access

Dystrophic epidermolysis with dilation of esophageal stricture: A case report

  • Authors:
    • Mengxi Wu
    • Jun Kuang
    • Jun Yan
    • Dongfang Li
    • Quanwei Guo
    • Xiaojia Zhu
    • Jianhua Zhang
  • View Affiliations / Copyright

    Affiliations: Department of Thoracic Surgery, Shenzhen Hospital, Southern Medical University, Shenzhen, Guangdong 518101, P.R. China
    Copyright: © Wu et al. This is an open access article distributed under the terms of Creative Commons Attribution License.
  • Article Number: 79
    |
    Published online on: December 28, 2023
       https://doi.org/10.3892/etm.2023.12367
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Abstract

Dystrophic epidermolysis bullosa (DEB) is a rare disease and the associated esophageal stricture is frequently complicated by the lack of clinical experience. The present study reported a very rare case of DEB in a 37‑year‑old male, who was admitted to Shenzhen Hospital (Shenzhen, China) due to an esophageal stricture. The patient received esophageal dilation under digital subtraction angiography. In this patient, dilation therapy was effective and safe. The patient underwent skin biopsies, and histological examination of the resected tissue specimens confirmed DEB diagnosis. The patient was followed up in the Department of Thoracic Surgery, Shenzhen Hospital, for 2 years without any recurrence of esophageal stricture. This is the first case report of dilation therapy in a very rare case of DEB with a satisfactory outcome, but the long‑term efficacy needs further observation. In addition, the latest relevant literature was reviewed and it was found that this treatment is uncommonly reported, as is the condition.
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Copy and paste a formatted citation
Spandidos Publications style
Wu M, Kuang J, Yan J, Li D, Guo Q, Zhu X and Zhang J: Dystrophic epidermolysis with dilation of esophageal stricture: A case report. Exp Ther Med 27: 79, 2024.
APA
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., & Zhang, J. (2024). Dystrophic epidermolysis with dilation of esophageal stricture: A case report. Experimental and Therapeutic Medicine, 27, 79. https://doi.org/10.3892/etm.2023.12367
MLA
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., Zhang, J."Dystrophic epidermolysis with dilation of esophageal stricture: A case report". Experimental and Therapeutic Medicine 27.2 (2024): 79.
Chicago
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., Zhang, J."Dystrophic epidermolysis with dilation of esophageal stricture: A case report". Experimental and Therapeutic Medicine 27, no. 2 (2024): 79. https://doi.org/10.3892/etm.2023.12367
Copy and paste a formatted citation
x
Spandidos Publications style
Wu M, Kuang J, Yan J, Li D, Guo Q, Zhu X and Zhang J: Dystrophic epidermolysis with dilation of esophageal stricture: A case report. Exp Ther Med 27: 79, 2024.
APA
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., & Zhang, J. (2024). Dystrophic epidermolysis with dilation of esophageal stricture: A case report. Experimental and Therapeutic Medicine, 27, 79. https://doi.org/10.3892/etm.2023.12367
MLA
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., Zhang, J."Dystrophic epidermolysis with dilation of esophageal stricture: A case report". Experimental and Therapeutic Medicine 27.2 (2024): 79.
Chicago
Wu, M., Kuang, J., Yan, J., Li, D., Guo, Q., Zhu, X., Zhang, J."Dystrophic epidermolysis with dilation of esophageal stricture: A case report". Experimental and Therapeutic Medicine 27, no. 2 (2024): 79. https://doi.org/10.3892/etm.2023.12367
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