Cancer of the supernumerary ovary in Mayer‑Rokitansty‑Küster‑Hauser Syndrome: A case report

Bae,Hyo  Sook; Ryu,Min  Ji; Kim,In  Sun; Kim,Sun  Haeng; Song,Jae  Yun

doi:10.3892/ol.2012.1073

February 2013 Volume 5 Issue 2

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February 2013 Volume 5 Issue 2

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Case Report

Cancer of the supernumerary ovary in Mayer‑Rokitansty‑Küster‑Hauser Syndrome: A case report

Authors:
- Hyo Sook Bae
- Min Ji Ryu
- In Sun Kim
- Sun Haeng Kim
- Jae Yun Song
View Affiliations / Copyright

Affiliations: Department of Obstetrics and Gynecology, Korea University Anam Hospital, Korea University College of Medicine, Sungbuk-gu, Seoul 136705, Republic of Korea, Department of Pathology, Korea University Anam Hospital, Korea University College of Medicine, Sungbuk-gu, Seoul 136705, Republic of Korea
Pages: 598-600
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Published online on: December 12, 2012

https://doi.org/10.3892/ol.2012.1073
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Abstract

Mayer-Rokitansty-Küster-Hauser (MRKH) syndrome is a Müllerian anomaly that presents with varying degrees of uterovaginal aplasia and is secondarily associated with cervicothoracic, auditory and skeletal anomalies. However, MRKH syndrome patients have normal and functional ovaries. A supernumerary ovary is an extremely rare form of an ectopic ovary and there are no reported cases of MRKH syndrome with cancer of the supernumerary ovary in the current literature. A 31-year-old female with a history of MRKH syndrome that was diagnosed 4 years previously presented with abdominal pain and a suspected malignant pelvic mass was identified. During the staging surgery, both ovaries were separated from the main mass, observed and removed. A third ovary was discovered in the pelvic mass and the diagnosis of primary ovarian cancer from the third ovary was confirmed by immunohistochemistry. We report the first known case of cancer of the supernumerary ovary in a patient with MRKH syndrome. Although both ovaries were confirmed to be normal in the patient with MRKH syndrome, we propose that an ovarian neoplasm should be considered in the diagnosis of a pelvic mass.

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Journals

International Journal of Molecular Medicine

International Journal of Oncology

Molecular Medicine Reports

Oncology Reports

Experimental and Therapeutic Medicine

Oncology Letters

Biomedical Reports

Molecular and Clinical Oncology

World Academy of Sciences Journal

International Journal of Functional Nutrition

International Journal of Epigenetics

Medicine International

Cancer of the supernumerary ovary in Mayer‑Rokitansty‑Küster‑Hauser Syndrome: A case report

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