Desmoplastic (collagenous) fibroma of the femur: A case report and review of the literature

Gao,Songtao; Cai,Qiqing; Yao,Weitao; Wang,Jiaqiang; Zhang,Peng; Wang,Xin

doi:10.3892/ol.2013.1535

Desmoplastic (collagenous) fibroma of the femur: A case report and review of the literature

Authors:
- Songtao Gao
- Qiqing Cai
- Weitao Yao
- Jiaqiang Wang
- Peng Zhang
- Xin Wang
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Affiliations: Department of Orthopedics of Henan Tumor Hospital, The Affiliated Tumor Hospital of Zhengzhou University, Zhengzhou, Henan 450008, P.R. China
Published online on: August 19, 2013 https://doi.org/10.3892/ol.2013.1535
Pages: 1285-1288

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Abstract

Desmoplastic fibroma is a rare, benign soft‑tissue tumor composed of spindled and stellate‑shaped cells that are embedded in a dense collagenous stroma. Clinically, desmoplastic fibroma presents as a firm, mobile, slow‑growing mass that is located in the subcutaneous tissue or near the deep aspect of the skeletal muscles. The present study describes the case of a 66‑year‑old female who presented with an inactive, firm, slightly tender mass in the lower medial segment of the right femur. An open biopsy was performed and the result of the pathological examination indicated a desmoplastic fibroma. The patient underwent a radical resection of the tumor and the accompanying bone, which was then reimplanted using devitalized tumor bone, self‑ilium graft and homologous allograft bone transplantation, with an internal fixation by locking the compression plate. This was followed by a reconstruction of the anterior and posterior cruciate ligaments and the lateral and medial collateral ligaments. There was no evidence of local recurrence at five years post‑surgery.

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