Atypical teratoid/rhabdoid tumor with hereditary multiple exostoses in an 18-year-old male: A case report

Wu,Qian; Xiao,Bo; Li,Li; Feng,Li

doi:10.3892/ol.2015.3389

September-2015 Volume 10 Issue 3

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September-2015 Volume 10 Issue 3

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Case Report

Atypical teratoid/rhabdoid tumor with hereditary multiple exostoses in an 18-year-old male: A case report

Authors:
- Qian Wu
- Bo Xiao
- Li Li
- Li Feng
View Affiliations / Copyright

Affiliations: Department of Neurology, Xiangya Hospital, Central South University, Changsha, Hunan 410008, P.R. China
Pages: 1561-1564
|
Published online on: June 17, 2015

https://doi.org/10.3892/ol.2015.3389
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Abstract

Atypical teratoid/rhabdoid tumor (AT/RT) is an aggressive embryonic brain tumor that is predominantly found in young children. The present study reports the unusual case of an adult male AT/RT patient with a history of another type of tumor, hereditary multiple exostoses (EXT or HME), who survived for 18 years. The patient's first and chief complaint was a 1‑month history of progressive projectile vomiting. The patient was admitted twice for treatment, and on the second admission, a craniotomy was performed to remove a intracranial mass. However, no radiotherapy or chemotherapy treatment was administered. Pathology revealed monotonous medium‑ to large‑sized neoplastic cells. The patient succumbed to a pulmonary infection and respiratory failure 14 days after the initial treatment. The prognosis for AT/RT is extremely poor; furthermore, the patient presented with another tumor. There may have been an association between the two tumors that worsened the clinical phenotype and prognosis of this patient. Additionally, symptomatic treatment for this condition is insufficient; early surgery and radiotherapy may be more useful for preventing the aggressive progression of these tumors.

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Journals

International Journal of Molecular Medicine

International Journal of Oncology

Molecular Medicine Reports

Oncology Reports

Experimental and Therapeutic Medicine

Oncology Letters

Biomedical Reports

Molecular and Clinical Oncology

World Academy of Sciences Journal

International Journal of Functional Nutrition

International Journal of Epigenetics

Medicine International

Atypical teratoid/rhabdoid tumor with hereditary multiple exostoses in an 18-year-old male: A case report

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