Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis (Review)

  • Authors:
    • Abdallah Abboud
    • Karim Masrouha
    • Maelle Saliba
    • Rachid Haidar
    • Raya Saab
    • Nabil Khoury
    • Ayman Tawil
    • Said Saghieh
  • View Affiliations

  • Published online on: March 4, 2021     https://doi.org/10.3892/ol.2021.12615
  • Article Number: 354
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Abstract

Extraskeletal Ewing sarcoma (EES) is a relatively uncommon primary tumor of the soft tissues, which accounts for 20‑30% of all reported cases of ES. Being uncommon, all members of the ES family tumors are treated following the same general protocol of sarcoma tumors. The present review summarizes the diagnosis, management and prognosis of EES, focusing on the differences between the subtypes of ESS. The clinical features and imaging of EES are also discussed. Magnetic resonance imaging is the modality of choice for diagnostic imaging and local staging, while core‑needle biopsy with pathological testing is used to obtain a definitive diagnosis. Although several oncology groups endorse that ES family of tumors should be treated with similar algorithm and protocols, some studies have demonstrated that surgery and radiotherapy may be used as a form of local control. However, further studies are required to conclude the optimum treatment option for EES.
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May-2021
Volume 21 Issue 5

Print ISSN: 1792-1074
Online ISSN:1792-1082

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Spandidos Publications style
Abboud A, Masrouha K, Saliba M, Haidar R, Saab R, Khoury N, Tawil A and Saghieh S: Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis (Review). Oncol Lett 21: 354, 2021
APA
Abboud, A., Masrouha, K., Saliba, M., Haidar, R., Saab, R., Khoury, N. ... Saghieh, S. (2021). Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis (Review). Oncology Letters, 21, 354. https://doi.org/10.3892/ol.2021.12615
MLA
Abboud, A., Masrouha, K., Saliba, M., Haidar, R., Saab, R., Khoury, N., Tawil, A., Saghieh, S."Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis (Review)". Oncology Letters 21.5 (2021): 354.
Chicago
Abboud, A., Masrouha, K., Saliba, M., Haidar, R., Saab, R., Khoury, N., Tawil, A., Saghieh, S."Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis (Review)". Oncology Letters 21, no. 5 (2021): 354. https://doi.org/10.3892/ol.2021.12615